Browsing by Author Evans, Sylvia M.

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Showing results 1 to 12 of 12
Issue DateTitleAuthor(s)
Jun-2021Cardiolipin Remodeling Defects Impair Mitochondrial Architecture and Function in a Murine Model of Barth Syndrome CardiomyopathyZhu, Siting; Chen, Ze'e; Zhu, Mason; Shen, Ying; Leon, Leonardo J.; Chi, Liguo; Spinozzi, Simone; Tan, Changming; Gu, Yusu; Nguyen, Anh; Zhou, Yi; Feng, Wei; Vaz, Frederic M.; Wang, Xiaohong; Gustafsson, Asa B.; Evans, Sylvia M.; Kunfu, Ouyang; Fang, Xi
2018Cell-Surface Marker Signature for Enrichment of Ventricular Cardiomyocytes Derived from Human Embryonic Stem CellsVeevers, Jennifer; Farah, Elie N.; Corselli, Mirko; Witty, Alec D.; Palomares, Karina; Vidal, Jason G.; Emre, Nil; Carson, Christian T.; Ouyang, Kunfu; Liu, Canzhao; van Vliet, Patrick; Zhu, Maggie; Hegarty, Jeffrey M.; Deacon, Dekker C.; Grinstein, Jonathan D.; Dirschinger, Ralf J.; Frazer, Kelly A.; Adler, Eric D.; Knowlton, Kirk U.; Chi, Neil C.; Martin, Jody C.; Chen, Ju; Evans, Sylvia M.
Feb-2023DELE1 is protective for mitochondrial cardiomyopathyHuynh, Helen; Zhu, Siting; Lee, Sharon; Bao, Yutong; Pang, Jing; Nguyen Anh; Gu, Yusu; Chen, Chao; Ouyang, Kunfu; Evans, Sylvia M.; Fang, Xi
20-Aug-2020Homozygous G650del nexilin variant causes in miceLiu, Canzhao; Spinozzi, Simone; Feng, Wei; Chen, Ze'e; Zhang, Lunfeng; Zhu, Siting; Wu, Tongbin; Fang, Xi; Ouyang, Kunfu; Evans, Sylvia M.; Chen, Ju
2014Loss of IP3R-dependent Ca2+ signalling in thymocytes leads to aberrant development and acute lymphoblastic leukemiaOuyang, Kunfu; Gomez-Amaro, Rafael Leandro; Stachura, David L.; Tang, Huayuan; Peng, Xiaohong; Fang, Xi; Traver, David; Evans, Sylvia M.; Chen, Ju
2017Loss-of-function mutations in co-chaperone BAG3 destabilize small HSPs and cause cardiomyopathyFang, Xi; Bogomolovas, Julius; Wu, Tongbin; Zhang, Wei; Liu, Canzhao; Veevers, Jennifer; Stroud, Matthew J.; Zhang, Zhiyuan; Ma, Xiaolong; Mu, Yongxin; Lao, Dieu-Hung; Dalton, Nancy D.; Gu, Yusu; Wang, Celine; Wang, Michael; Liang, Yan; Lange, Stephan; Ouyang, Kunfu; Peterson, Kirk L.; Evans, Sylvia M.; Chen, Ju
Sep-2021Mediator complex proximal Tail subunit MED30 is critical for Mediator core stability and cardiomyocyte transcriptional networkTan, Changming; Zhu, Siting; Chen, Zee; Liu, Canzhao; Li, Yang E.; Zhu, Mason; Zhang, Zhiyuan; Zhang, Zhiwei; Zhang, Lunfeng; Gu, Yusu; Liang, Zhengyu; Boyer, Thomas G.; Ouyang, Kunfu; Evans, Sylvia M.; Fang, Xi
27-Sep-2022Mitochondrial Stress Induces an HRI-eIF2 alpha Pathway Protective for CardiomyopathyZhu, Siting; Nguyen, Anh; Pang, Jing; Zhao, Jun; Chen, Ze'e; Liang, Zhengyu; Gu, Yusu; Huynh, Helen; Bao, Yutong; Lee, Sharon; Kluger, Yuval; Ouyang, Kunfu; Evans, Sylvia M.; Fang, Xi
2019Nexilin Is a New Component of Junctional Membrane Complexes Required for Cardiac T-Tubule FormationLiu, Canzhao; Spinozzi, Simone; Chen, Zia-Yu; Fang, Xi; Feng, Wei; Perkins, Guy; Cattaneo, Paola; Guimaraes-Camboa, Nuno; Dalton, Nancy D.; Peterson, Kirk L.; Wu, Tongbin; Ouyang, Kunfu; Fu, Xiang-Dong; Evans, Sylvia M.; Chen, Ju
Jul-2020Nexilin Is Necessary for Maintaining the Transverse-Axial Tubular System in Adult CardiomyocytesSpinozzi, Simone; Liu, Canzhao; Chen, Ze'e; Feng, Wei; Zhang, Lunfeng; Ouyang, Kunfu; Evans, Sylvia M.; Chen, Ju
2011Selective deletion of long but not short Cypher isoforms leads to late-onset dilated cardiomyopathyCheng, Hongqiang; Zheng, Ming; Peter, Angela K.; Kimura, Kensuke; Li, Xiaodong; Ouyang, Kunfu; Shen, Tao; Cui, Li; Frank, Derk; Dalton, Nancy D.; Gu, Yusu; Frey, Norbert; Peterson, Kirk L.; Evans, Sylvia M.; Knowlton, Kirk U.; Sheikh, Farah; Chen, Ju
2014Targeted Ablation of Nesprin 1 and Nesprin 2 from Murine Myocardium Results in Cardiomyopathy, Altered Nuclear Morphology and Inhibition of the Biomechanical Gene ResponseBanerjee, Indroneal; Zhang, Jianlin; Moore-Morris, Thomas; Pfeiffer, Emily; Buchholz, Kyle S.; Liu, Ao; Ouyang, Kunfu; Stroud, Matthew J.; Gerace, Larry; Evans, Sylvia M.; McCulloch, Andrew; Chen, Ju